Etiqueta: PediPath
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Angiomatous fibrous histiocytoma
A relatively new tumor described in 1979, primarily affecting children and young adults, typically occurs in the deep dermis or subcutaneous tissue, resembling hematomas. With low malignant potential, it shows EWSR1 gene rearrangement in many cases. Its rare nature and overlapping features with other tumors highlight the need for awareness.
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Single Umbilical Artery
The normal umbilical cord has two arteries and one vein, that being said Absence of one of the umbilical arteries can happen -how often you may ask-, not that often roughly in 0.5-5% of neonates (depending on the filters applied) But we can use 1% as a mnemonic value. In 10-27% of cases the fetus…
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Wilms Tumor (Nephroblastoma)
Named in honor of Max Wilms (who originally proposed the origin of mixed kidney tumors) Originated from nephrogenic blastema 90% of kidney pediatric tumors Frequently present WT1 alterations (11p13) Associated with syndromes (10%): Beckwith-Wiedemann, Denysh-Drash, WAGR Palpable Painless mass is usually the most frequent presentation Well circumscribed, pseudo encapsulated, gray-tan. Can have cystic areas Usually…
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